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Cystic Fibrosis in Focus

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Cystic Fibrosis: The Essential Role of Pancreatic Enzyme Replacement Therapy in Patient Care

Host: John J. Russell, MD Guest: Suzanne Michel, MPH, RD, LDN Approximately 85-90% of patients with Cystic Fibrosis suffer from pancreatic insufficiency since birth, which significantly complicates the disease and adversely affects both quality of life and life expectancy. Join Professor Suzanne Michele, registered dietitian, as she discusses supplemental enzymes and their role in the health of persons who have CF, the barriers to adherence with pancreatic enzyme replacement therapy, and...

Duration: 00:18:29

Chronic Care Challenges with Cystic Fibrosis

Host: Barnett Mennen, MD Guest: Peter J. Mogayzel, Jr, MD, PhD, MBA This activity discusses the etiology of cystic fibrosis lung disease, the current clearance approaches and the role CFTR modulator therapy in the treatment of cystic fibrosis lung disease, and the relationship between lung function and nutritional status in cystic fibrosis.

Duration: 00:13:29

Lung Transplantation for Cystic Fibrosis

Host: Barnett Mennen, MD Guest: Denis Hadjiliadis, MD, MHS, PhD Lung Transplantation is often considered for patients with cystic fibrosis. In this activity, we will discuss how patients are evaluated and listed, common complications, medications that are used, and survival after lung transplantation.

Duration: 00:18:29

Mental Health Screening: Cystic Fibrosis Foundation Guidelines and Specific Recommendations: The Benefits and Risks

Host: Barnett Mennen, MD Guest: Erin McElroy Barker, LCSW Patients with cystic fibrosis and their families are at a higher risk for mental health issues which have been associated with other complications. In this activity, Ms. McElroy Barker will discuss how the CF community recognized the need for mental health services and the guidelines the CF Foundation recommends for screening patients.

Duration: 00:14:29

Rationale for Performing Airway Clearance for Patients with Cystic Fibrosis

Host: Jennifer Caudle, DO Guest: Robert L. Zanni, MD, CPI Airway clearance is the primary therapy for patients with cystic fibrosis. In this activity, Dr. Zanni will discuss the rationale for performing airway clearance, as well as current mechanical and pharmacologic choices for patients. He will also discuss airway clearance therapies that are making their way through the pipeline.

Duration: 00:10:59

Cell Death and Differentiation: A Novel Treatment of Cystic Fibrosis Acting On-Target

A novel treatment of cystic fibrosis acting on-target: cysteamine plus epigallocatechin gallate for the autophagy-dependent rescue of class II-mutated CFTR Tosco A1, De Gregorio F1, Esposito S2, De Stefano D2, Sana I2, Ferrari E2, Sepe A1, Salvadori L1, Buonpensiero P1, Di Pasqua A1, Grassia R3, Leone CA3,Guido S4, De Rosa G5, Lusa S6, Bona G7, Stoll G8,9,10,11, Maiuri MC9, Mehta A12, Kroemer G9,13,14,15,16,17, Maiuri L2,7, Raia V1. Cell Death Differ. 2016 Aug;23(8):1380-93. doi:...

Duration: 00:03:30

Journal of Cystic Fibrosis: Microbial Colonization and Lung Function in Adolescents With Cystic Fibrosis

Microbial colonization and lung function in adolescents with cystic fibrosis Hector A1, Kirn T1, Ralhan A1, Graepler-Mainka U1, Berenbrinker S1, Riethmueller J1, Hogardt M2, Wagner M3, Pfleger A3, Autenrieth I4, Kappler M5, Griese M5, Eber E3, Martus P6, Hartl D7. J Cyst Fibros. 2016 May;15(3):340-9. doi: 10.1016/j.jcf.2016.01.004. Epub 2016 Feb 5. Interpretation: Patients with cystic fibrosis suffer from chronic progressive pulmonary disease, driven by cycles of airway infection and...

Duration: 00:02:30